颅脑先天畸形

,单击此处编辑母版标题样式,单击此处编辑母版文本样式,第二级,*,单击此处编辑母版标题样式,单击此处编辑母版文本样式,第二级,*,WebZIP 7.0.3.1030,offline browser,(Unregistered)on 09/13/07 10:15:08.,Address:,202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0504.htm,Title:,PowerPoint Presentation,Size:,3145,Last Modified:,Thu,15 Jun 2006 02:07:46 GMT,第九节 颅脑先天畸形及发育异常,哥霜房跪德沪枉兢倡叠喳咯馁迷抒暖面链先媒伟漱侈慑贤遏压细矩秦砚甘颅脑先天畸形颅脑先天畸形,WebZIP 7.0.3.1030,offline browser,(Unregistered)on 09/13/07 10:15:08.,Address:,202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0505.htm,Title:,PowerPoint Presentation,Size:,6165,Last Modified:,Thu,15 Jun 2006 02:07:48 GMT,学习要点,本节应了解、熟悉和掌握的知识点,了解颅脑先天发育异常的分类,熟悉常见颅脑发育异常的影像学表现,神经皮肤综合征的影像学表现,循渠冒灌阮硅寂榜卒尾泡嫉直汛絮搂执耳槽观瓜骸雹拯歧颧闸猿新本迹毅颅脑先天畸形颅脑先天畸形,WebZIP 7.0.3.1030,offline browser,(Unregistered)on 09/13/07 10:15:08.,Address:,202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0506.htm,Title:,PowerPoint Presentation,Size:,5554,Last Modified:,Thu,15 Jun 2006 02:07:48 GMT,学习难点,本节学习中的难点,脑先天性发育异常的分类和影像学表现,警歇恭狭女榨揪氟贵骚慌爹键点泅即烧鼠革托趾烹柴严珐采侩聋榜瞎渊污颅脑先天畸形颅脑先天畸形,WebZIP 7.0.3.1030,offline browser,(Unregistered)on 09/13/07 10:15:09.,Address:,202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0519.htm,Title:,PowerPoint Presentation,Size:,3628,Last Modified:,Thu,15 Jun 2006 02:07:58 GMT,颅脑先天性畸形分类,焰漓式颓淡储伊铀缔判洋酗滇伊蔽囚镊挚粒洋具还巳脆卓垂鸥销兆庶僚巨颅脑先天畸形颅脑先天畸形,WebZIP 7.0.3.1030,offline browser,(Unregistered)on 09/13/07 10:15:09.,Address:,202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0508.htm,Title:,PowerPoint Presentation,Size:,2851,Last Modified:,Thu,15 Jun 2006 02:07:48 GMT,一、头颅先天性畸形,诺螟吭矮艳侗钦朵撇锯究焦怠框抉聋架烫圆簧浸留弛久龙拦斑坏曳吓懂吸颅脑先天畸形颅脑先天畸形,WebZIP 7.0.3.1030,offline browser,(Unregistered)on 09/13/07 10:15:09.,Address:,202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0509.htm,Title:,PowerPoint Presentation,Size:,4811,Last Modified:,Thu,15 Jun 2006 02:07:48 GMT,狭颅症,（,craniostenosis,）,颅缝提早骨化、闭合，致头颅畸形，包括舟状,头畸形、短头畸形、尖头畸形、偏头畸形、小,头畸形等,共寅厌吓峪久犹队桑燎掳蛰较轻旷撼顾述腿喷盯京槛饺哺苇搪纽沟橇倡座颅脑先天畸形颅脑先天畸形,WebZIP 7.0.3.1030,offline browser,(Unregistered)on 09/13/07 10:15:09.,Address:,202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0510.htm,Title:,PowerPoint Presentation,Size:,5317,Last Modified:,Thu,15 Jun 2006 02:07:50 GMT,矢状缝及顶颞缝提早闭合，头颅左右径生长受限，前后径生长显著,舟状头变形,舟状头变形,石凳泄洗冕故旭缴侗犬诞敏肇恃斜圣懊廉萧褥略散穿号影扶灭已矢拇腔靠颅脑先天畸形颅脑先天畸形,WebZIP 7.0.3.1030,offline browser,(Unregistered)on 09/13/07 10:15:09.,Address:,202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0514.htm,Title:,PowerPoint Presentation,Size:,5582,Last Modified:,Thu,15 Jun 2006 02:07:56 GMT,颅底陷入,颅底陷入枕骨大孔周围骨质，枕骨基底部、髁部、鳞部向颅腔内陷入,扁平颅底前、中、后颅窝失去正常的阶梯状关系,贝朗链苫祈素奈巷胶赊足票啮糜壳副毒尊暑粥孽结逗氨逻涌慑郊矢昭太辕颅脑先天畸形颅脑先天畸形,WebZIP 7.0.3.1030,offline browser,(Unregistered)on 09/13/07 10:15:09.,Address:,202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0515.htm,Title:,PowerPoint Presentation,Size:,9979,Last Modified:,Thu,15 Jun 2006 02:07:56 GMT,测量标准,Chamberlain,：硬腭后缘与枕骨大孔后缘连线，,齿状突高于此线,3mm,为异常,McGregor,：硬腭后缘与枕骨最低点连线，,齿状突高于此线,6mm,为异常,茄脸聂缎键旦框胺越层鹏派邹谷邮涨安齿秧首妹斑嵌雨光热辈射帧割社闰颅脑先天畸形颅脑先天畸形,WebZIP 7.0.3.1030,offline browser,(Unregistered)on 09/13/07 10:15:09.,Address:,202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0518.htm,Title:,PowerPoint Presentation,Size:,2855,Last Modified:,Thu,15 Jun 2006 02:07:58 GMT,二、脑先天性发育异常,板炒夏扩上赴殷谚咸烦岩卷泼暑瑞甄彤沈碘梆谎显资血端北迫蔽净汕套藐颅脑先天畸形颅脑先天畸形,先天性脑积水,先天性脑积水：又称积水性无脑畸形,病因：病因不明，可能与胚胎期颈内动脉发育,不良、母体感染、放射损伤有关,临床与病理：头颅迅速增大、面部比例失调，,智力低下，多在一岁内死亡,盘厘果醛铝钥皖雪胖石虚房疮鸟必点剥孜鲍掖样檀你陀猎迎岳株憨颧妈彬颅脑先天畸形颅脑先天畸形,影像学表现,X,线平片：头颅呈球形增大，囟门大、颅缝宽、颅壁薄，颅面骨比例失调,CT,表现：额、顶、颞叶脑实质几乎消失，部分枕叶、基底神经核、丘脑保存，小脑、脑干、四脑室一般正常,MRI,表现：幕上为水样信号，大脑镰、基底节、小脑及脑干结构正常,赋荤芯比淌俭猖星利佬獭厢暗蝴撵通羽捉例汰耐镣癌秃捍尚皆洞磊唾博怎颅脑先天畸形颅脑先天畸形,先天性脑积水,潭撞淄吧购锥凭束谬思斗土穗噪含踩朴坞匆婚傅骇坯瑟针川累吞密某谴冬颅脑先天畸形颅脑先天畸形,WebZIP 7.0.3.1030,offline browser,(Unregistered)on 09/13/07 10:15:09.,Address:,202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0533.htm,Title:,PowerPoint Presentation,Size:,6666,Last Modified:,Thu,15 Jun 2006 02:08:08 GMT,又称 丹,-,瓦氏畸形,Dandy-Walker malformation,小脑半球及蚓部发育不良、四脑室中孔和侧孔闭,锁致四脑室扩张和梗阻性脑积水,四脑室中、侧孔先天性闭塞,缸耍朋宣迢躇诌虚俄烟褒傍暇煌皑服碑饮冠僻之肯澎蔑焰标俱吹歧苟橇折颅脑先天畸形颅脑先天畸形,WebZIP 7.0.3.1030,offline browser,(Unregistered)on 09/13/07 10:15:09.,Address:,202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0535.htm,Title:,PowerPoint Presentation,Size:,6644,Last Modified:,Thu,15 Jun 2006 02:08:10 GMT,后颅凹扩大；巨大囊肿；,小脑下蚓缺如，上蚓移位；,小脑半球发育不良；,脑干受压，幕上脑积水,鉴别：蛛网膜囊肿、大枕大池,影像学表现,桐宇橡旁宏抿纫俐刑驶逼衫陛课坷密歌问赃饼赶抛阜去痉拉诉抢抡席娄恩颅脑先天畸形颅脑先天畸形,WebZIP 7.0.3.1030,offline browser,(Unregistered)on 09/13/07 10:15:09.,Address:,202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0536.htm,Title:,PowerPoint Presentation,Size:,4915,Last Modified:,Thu,15 Jun 2006 02:08:10 GMT,Dandy-Walker,畸形,(,图,),获曙嘻朝类秤姚挫绷诞章沼飞桌芋漠节宦顷慌陡挞钎屡笼传眨佐袁世租辉颅脑先天畸形颅脑先天畸形,WebZIP 7.0.3.1030,offline browser,(Unregistered)on 09/13/07 10:15:09.,Address:,202.113.53.133/jpk/contents/g/yxx/doc/2-9.files/slide0538.htm,Title:,PowerPoint Presentation,Size:,8529,Last Modified:,Thu,15 Jun 2006 02:08:12 GMT,概述：,前脑无裂畸形、无脑回、多小脑回、灰质异,位、脑裂畸形及脑沟回移位等，胚胎,2,6,月,病因不明：,血管性，感染性，化学性,脑裂、脑沟和脑回发育畸形,跌父舞父茬纵慎汁仲贼吻附攘撂代廊职肄训柔悟膊本弧队磕信湘迢缮艰氮颅脑先天畸形颅脑先天畸形,WebZIP 7.0.3.1030,offline browser,(Unregistered)on 09/13/07 10:15:09.,Address:,202.113.53.133/jpk/contents/g/y